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2019, Volume 35, Number 1, Page(s) 055-057     
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DOI: 10.5146/tjpath.2015.01362
Tricuspid Valve Hemangioma Associated with Hypoplastic Left Heart Syndrome Presenting as Sudden Infant Death Syndrome
Brijnandan GUPTA1, Shouriyo GHOSH2, Maikal KUJUR3, Khushbu KHETAN2, Tarun KUMAR2
1Department of Pathology, Lady Hardinge Medical College, NEW DELHI, India
2All India Institute of Medical Sciences, NEW DELHI, India
3Chhattisgarh Institute of Medical Sciences, Bilaspur, CHHATTISGARH, India
Keywords: Tricuspid valve, Hemangioma, Hypoplastic left heart syndrome, Sudden infant death syndrome

Primary cardiac tumors are rare in children with a low incidence varying from 0.0017 to 0.28% in autopsy studies. Approximately 90% of the reported primary cardiac tumors in the pediatric population are benign and the most common subtype is rhabdomyomas accounting for approximately 60%, while hemangiomas are rare primary tumors with a 5% incidence. Hypoplastic left heart syndrome is abnormal development of the left-sided cardiac structures, leading to obstruction of blood flow from the left ventricle out-flow tract. Here we report a case of tricuspid hemangioma in association with hypoplastic left heart syndrome, a rare association not previously reported in the literature.

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