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2019, Volume 35, Number 3, Page(s) 258-262
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DOI: 10.5146/tjpath.2017.01411 |
Concomitant Intraocular Retinoblastoma and Choroidal Hemangioma in a 1-Year-Old Boy |
Yacoub A. YOUSEF1, Maysa AL-HUSSAİNİ2, Fareed H. BARAKAT2, Alaa SALEH3, Mona MOHAMMAD1, Rasha DEEBAJAH4 |
1Department of Surgery/Ophthalmology, King Hussein Cancer Center, AMMAN, JORDAN
2Department of Pathology, King Hussein Cancer Center, AMMAN, JORDAN
3Department of Radiology, King Hussein Cancer Center, AMMAN, JORDAN
4Department of Pediatric Oncology, King Hussein Cancer Center, AMMAN, JORDAN |
Keywords:
Choroidal neoplasm, Hemangioma, Leukocoria, Retinoblastoma |
We report a case of concomitant choroidal hemangioma in an eye that harbored intraocular retinoblastoma (RB) in a 1-year-old child. A
12-month-old boy presented with right white pupil (Leukocoria). The initial clinical diagnosis was unilateral intraocular RB Group C. The
eye was treated initially by systemic chemotherapy combined with focal consolidation therapy followed by I-125 plaque radiotherapy. Massive
sub-retinal recurrence was seen 4 months later, and Magnetic Resonance Imaging (MRI) showed extra-scleral invasion of the tumor, and
therefore enucleation was performed. Microscopic examination revealed a differentiated retinoblastoma associated at the site of the base of the
tumor with choroidal hemangioma with trans-scleral invasion. Orbit MRI was repeated 3 months after the surgery, and there was no orbital
tumor recurrence. We are reporting a rare case of pathologically concomitant choroidal hemangioma with trans-scleral invasion in an eye that
harbored active recurrent intraocular RB. This trans-scleral extension of hemangioma was misinterpreted by MRI as extraocular retinoblastoma
and resulted in enucleation.
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